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Frontometaphyseal Dysplasia 2

Disease ID: disease_node_15702

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DbxrefMIM:617137
SubclassofDOID_0050736, DOID_0111785
Data SourceDOID
SynonymsFMD2
Doid Labelfrontometaphyseal dysplasia 2
Doid DescriptionA frontometaphyseal dysplasia characterized by generalized skeletal dysplasia, deafness, urogenital defects and an increased tendency to form keloid scars that has_material_basis_in heterozygous mutation in MAP3K7 on chromosome 6q15.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15702
Doid IdDOID_0111787
LabelFrontometaphyseal Dysplasia 2