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Spondyloepiphyseal Dysplasia Nishimura Type

Disease ID: disease_node_15685

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DbxrefMIM:618618
SubclassofDOID_0050736, DOID_0112280
Data SourceDOID
SynonymsSEDN
Doid Labelspondyloepiphyseal dysplasia Nishimura type
Doid DescriptionA spondyloepiphyseal dysplasia characterized by disproportionate short stature with short limbs, small hands and feet, midface hypoplasia with a small nose, mild spondylar dysplasia, delayed epiphyseal ossification of the hip and knee, and severe brachydactyly with cone-shaped phalangeal epiphyses that has_material_basis_in heterozygous gain-of-function mutation in the MIR140 gene on chromosome 16q22.1.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15685
Doid IdDOID_0112288
LabelSpondyloepiphyseal Dysplasia Nishimura Type