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Otospondylomegaepiphyseal Dysplasia, Autosomal Recessive

Disease ID: disease_node_15674

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DbxrefMIM:215150
SubclassofDOID_2256, DOID_0050737
Data SourceDOID
SynonymsCHONDRODYSTROPHY WITH SENSORINEURAL DEAFNESS, NANCE-INSLEY SYNDROME, NANCE-SWEENEY CHONDRODYSPLASIA, OSMEDB
Disease Has LocationUBERON_0001437
Doid Labelotospondylomegaepiphyseal dysplasia, autosomal recessive
Doid DescriptionAn osteochondrodysplasia that results from mutations autosomal recessive inheritance of mutations in the COL11A2 gene which results_in enlargement of the located_in epiphysis in located_in hand and located_in foot, distinct facial features, platyspondyly and hearing loss. OMIM mapping confirmed by DO. [SN].
Has PhenotypeHP_0000926
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15674
Doid IdDOID_0080026
LabelOtospondylomegaepiphyseal Dysplasia, Autosomal Recessive