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Silverman-Handmaker Type Dyssegmental Dysplasia

Disease ID: disease_node_15648

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DbxrefICD10CM:Q77.7, MIM:224410, ORDO:1865
SubclassofDOID_2256, DOID_0050737
Data SourceDOID
Doid LabelSilverman-Handmaker type dyssegmental dysplasia
Doid DescriptionAn osteochondrodysplasia characterized by short-limbed dwarfism, anisospondyly, and neonatal lethality that has_material_basis_in autosomal recessive inheritance of homozygous or compound heterozygous mutation in the gene encoding perlecan (HSPG2) on chromosome 1p36.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15648
Doid IdDOID_0090032
LabelSilverman-Handmaker Type Dyssegmental Dysplasia