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Osteogenesis Imperfecta Type 21

Disease ID: disease_node_15616

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DbxrefMIM:619131
SubclassofDOID_12347, DOID_0050737
Data SourceDOID
SynonymsOI21, osteogenesis imperfecta type XXI
Doid Labelosteogenesis imperfecta type 21
Doid DescriptionAn osteogenesis imperfecta characterized by multiple fractures that often occur after minor trauma, disproportionate short stature, and scoliosis that has_material_basis_in homozygous or compound heterozygous mutation in KDELR2 on chromosome 7p22.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15616
Doid IdDOID_0112201
LabelOsteogenesis Imperfecta Type 21