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Familial Behcet-Like Autoinflammatory Syndrome

Disease ID: disease_node_15593

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DbxrefMIM:616744
SubclassofDOID_0050736, DOID_0051000
Data SourceDOID
SynonymsA20 haploinsufficiency
Doid Labelfamilial Behcet-like autoinflammatory syndrome
Doid DescriptionAn autoinflammatory disease that is characterized by characterized by ulceration of mucosal surfaces, particularly in the oral and genital areas and that has_material_basis_in heterozygous mutation in the TNFAIP3 gene on chromosome 6q23.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15593
Doid IdDOID_0080944
LabelFamilial Behcet-Like Autoinflammatory Syndrome