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Familial Cold Autoinflammatory Syndrome 1

Disease ID: disease_node_15592

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DbxrefICD10CM:L50.2, MIM:120100, ORDO:47045
SubclassofDOID_0050736, DOID_0090061
Data SourceDOID
SynonymsFCAS1
Doid Labelfamilial cold autoinflammatory syndrome 1
Doid DescriptionA familial cold autoinflammatory syndrome characterized by autosomal domit inheritance that has_material_basis_in heterozygous mutation in the NLRP gene on chromosome 1q44.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15592
Doid IdDOID_0090062
LabelFamilial Cold Autoinflammatory Syndrome 1