This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Tnf Receptor–Associated Periodic Syndrome

Disease ID: disease_node_15588

Connections displayed (default: 10).
Loading graph...

DbxrefGARD:8457, ICD10CM:E85.0, MIM:142680, ORDO:32960
SubclassofDOID_0050736, DOID_0051000
Data SourceDOID
SynonymsFHF, FPF, TRAPS, autosomal dominant familial periodic fever, familial Hibernian fever, hibernian fever, tumor necrosis factor receptor associated periodic syndrome
Doid LabelTNF receptor–associated periodic syndrome
Doid DescriptionAn autoinflammatory disease characterized by recurrent fever, abdominal pain, localized tender skin lesions, arthralgia and myalgia associated with skin, joint, ocular and serosal inflammation that has_material_basis_in heterozygous mutation in the TNFRSF1A gene on chromosome 12p13. nomenclature change.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15588
Doid IdDOID_0090018
LabelTnf Receptor–Associated Periodic Syndrome