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Caroli Syndrome

Disease ID: disease_node_15475

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DbxrefGARD:6002
SubclassofDOID_272, DOID_225, DOID_0050737, DOID_866, DOID_4138
Data SourceDOID
Disease Has LocationUBERON_0002017, UBERON_0002107, UBERON_0002394
Doid LabelCaroli syndrome
Doid DescriptionA syndrome that is characterized by the presence of associated congenital hepatic fibrosis and that is associated with autosomal recessive polycystic kidney disease.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15475
Doid IdDOID_0081394
LabelCaroli Syndrome