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Familial Erythrocytosis 2

Disease ID: disease_node_15335

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DbxrefICD10CM:D75.1, MIM:263400, ORDO:238557
SubclassofDOID_0050737, DOID_10780
Data SourceDOID
SynonymsChuvash erythromatosis, Chuvash polycythemia, Chuvash type polycythemia, ECYT2, autosomal recessive benign erythrocytosis
Doid Labelfamilial erythrocytosis 2
Doid DescriptionA primary polycythemia that has_material_basis_in homozygous or compound heterozygous mutation in the VHL gene (608537) on chromosome 3p25.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15335
Doid IdDOID_0060474
LabelFamilial Erythrocytosis 2