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Familial Erythrocytosis 8

Disease ID: disease_node_15330

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DbxrefMIM:222800, ORDO:714
SubclassofDOID_10780
Data SourceDOID
SynonymsBPGM deficiency, DPGM deficiency, ECYT8, bisphosphoglycerate mutase deficiency, bisphosphoglyceromutase deficiency, diphosphoglycerate mutase deficiency of erythrocyte, hemolytic anemia due to diphosphoglycerate mutase deficiency
Doid Labelfamilial erythrocytosis 8
Doid DescriptionA primary polycythemia characterized by erythrocytosis and in some cases hemolytic anemia that has_material_basis_in homozygous or compound heterozygous mutation in the BPGM gene on chromosome 7q33.
Disease Node Iddisease_node_15330
Doid IdDOID_0111630
LabelFamilial Erythrocytosis 8