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Familial Erythrocytosis 6

Disease ID: disease_node_15328

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DbxrefMIM:617980
SubclassofDOID_10780
Data SourceDOID
SynonymsECYT6, beta-globin type erythrocytosis, beta-globin type polycythemia
Doid Labelfamilial erythrocytosis 6
Doid DescriptionA primary polycythemia characterized by high oxygen affinity hemoglobin and compensatory polycythemia that has_material_basis_in heterozygous mutation in HBB on chromosome 11p15.4.
Disease Node Iddisease_node_15328
Doid IdDOID_0111632
LabelFamilial Erythrocytosis 6