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Congenital Dyserythropoietic Anemia Type Iva

Disease ID: disease_node_15271

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DbxrefMIM:613673, NCI:C157148, ORDO:293825, SNOMEDCT_US_2023_03_01:719453009, UMLS_CUI:C3150926
SubclassofDOID_0050736, DOID_1338
Data SourceDOID
SynonymsCDA IV, CDA due to KLF1 mutation, CDA type 4, CDA type IV, CDAN4, Congenital dyserythropoietic anaemia due to KLF1 mutation, Congenital dyserythropoietic anaemia type 4, Congenital dyserythropoietic anemia due to KLF1 mutation, Congenital dyserythropoietic anemia type 4, congenital dyserythropoietic anaemia type IV
Doid Labelcongenital dyserythropoietic anemia type IVa
Doid DescriptionA congenital dyserythropoietic anemia characterized by ineffective erythropoiesis and hemolysis resulting in anemia and abnormal erythroblast morphology that has_material_basis_in heterozygous mutation in the KLF1 gene on chromosome 19p13.13.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15271
Doid IdDOID_0111400
Disease Has Basis InHP_0001197
LabelCongenital Dyserythropoietic Anemia Type Iva