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Sideroblastic Anemia 5

Disease ID: disease_node_15254

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DbxrefMIM:619523
SubclassofDOID_0050737, DOID_8955
Data SourceDOID
SynonymsSIDBA5
Doid Labelsideroblastic anemia 5
Doid DescriptionA sideroblastic anemia that is characterized by abnormal iron accumulation in the mitochondria or erythroid cells that has_material_basis_in compound heterozygous mutation in the HSCB gene on chromosome 22q12. Only 1 patient has been reported, 11/12/2024.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15254
Doid IdDOID_0061007
LabelSideroblastic Anemia 5