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Autosomal Domit Auditory Neuropathy 1

Disease ID: disease_node_15132

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DbxrefICD10CM:H90.3, MIM:609129
SubclassofDOID_0050564
Data SourceDOID
SynonymsAUNA1, NSDAN, nonsyndromic dominant auditory neuropathy
Doid Labelautosomal domit auditory neuropathy 1
Doid DescriptionAn autosomal domit nonsyndromic deafness characterized by preservation of outer hair cell function and abnormal or absent auditory brainstem responses that has_material_basis_in heterozygous mutation in the DIAPH3 gene on chromosome 13q.
Disease Node Iddisease_node_15132
Doid IdDOID_0060690
LabelAutosomal Domit Auditory Neuropathy 1