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Autosomal Domit Nonsyndromic Deafness 87

Disease ID: disease_node_15122

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DbxrefMIM:620281
SubclassofDOID_0050564
Data SourceDOID
SynonymsDFNA87, autosomal dominant deafness 87
Doid Labelautosomal domit nonsyndromic deafness 87
Doid DescriptionAn autosomal domit nonsyndromic deafness characterized by prelingual profound sensorineural hearing loss with inner ear anomalies, including cochlear maldevelopment, absence of the osseous spiral lamina, and/or an enlarged vestibular aqueduct that has_material_basis_in heterozygous mutation in the PI4KB gene on chromosome 1q21.
Disease Node Iddisease_node_15122
Doid IdDOID_0070606
LabelAutosomal Domit Nonsyndromic Deafness 87