This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Autosomal Domit Nonsyndromic Deafness 86

Disease ID: disease_node_15118

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:620280
SubclassofDOID_0050564
Data SourceDOID
SynonymsDFNA86, autosomal dominant deafness 86
Doid Labelautosomal domit nonsyndromic deafness 86
Doid DescriptionAn autosomal domit nonsyndromic deafness characterized by late-onset progressive hearing loss through p53-mediated hair cell apoptosis that has_material_basis_in heterozygous mutation in the THOC1 gene on chromosome 18p11. Only one family reported as of 2024-09-20.
Disease Node Iddisease_node_15118
Doid IdDOID_0070610
LabelAutosomal Domit Nonsyndromic Deafness 86