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Autosomal Domit Nonsyndromic Deafness 1

Disease ID: disease_node_15115

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DbxrefICD10CM:H90.3, MIM:124900
SubclassofDOID_0050564
Data SourceDOID
SynonymsDFNA1, Konigsmark syndrome, LFHL1, autosomal dominant deafness 1, autosomal dominant deafness 1, with or without thrombocytopenia, hereditary low frequency hearing loss 1
Doid Labelautosomal domit nonsyndromic deafness 1
Doid DescriptionAn autosomal domit nonsyndromic deafness that is characterized by low frequency progressive hearing loss and has_material_basis_in mutation in the DIAPH1 gene on chromosome 5q31.
Disease Node Iddisease_node_15115
Doid IdDOID_0110541
LabelAutosomal Domit Nonsyndromic Deafness 1