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Autosomal Domit Nonsyndromic Deafness 51

Disease ID: disease_node_15079

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DbxrefICD10CM:H90.3, MIM:613558
SubclassofDOID_0050564, DOID_0060429
Data SourceDOID
SynonymsDFNA51, autosomal dominant deafness 51, chromosome 9q21.11 duplication syndrome
Doid Labelautosomal domit nonsyndromic deafness 51
Doid DescriptionAn autosomal domit nonsyndromic deafness that is characterized by postlingual onset in the fourth decade of life with high frequency progressive hearing loss and has_material_basis_in a 269-kb duplication of chromosome 9q21.11 involving the TJP2 and FAM189A2 genes.
Disease Node Iddisease_node_15079
Doid IdDOID_0110577
LabelAutosomal Domit Nonsyndromic Deafness 51