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Autosomal Recessive Nonsyndromic Deafness 100

Disease ID: disease_node_14970

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DbxrefMIM:618422
SubclassofDOID_0050565
Data SourceDOID
SynonymsDFNB100, autosomal recessive deafness 100
Doid Labelautosomal recessive nonsyndromic deafness 100
Doid DescriptionAn autosomal recessive nonsyndromic deafness characterized by prelingual onset of profound sensorineural deafness without vestibular involvement that has_material_basis_in homozygous or compound heterozygous mutation in the PPIP5K2 gene on chromosome 5q21.1.
Disease Node Iddisease_node_14970
Doid IdDOID_0111638
LabelAutosomal Recessive Nonsyndromic Deafness 100