This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Autosomal Recessive Nonsyndromic Deafness 109

Disease ID: disease_node_14969

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:618013
SubclassofDOID_0050565
Data SourceDOID
SynonymsDFNB109, autosomal recessive deafness 109
Doid Labelautosomal recessive nonsyndromic deafness 109
Doid DescriptionAn autosomal recessive nonsyndromic deafness characterized by bilateral congenital severe to profound sensorineural hearing loss and vestibular dysplasia without balance or movement issues that has_material_basis_in homozygous or compound heterozygous mutation in the ESRP1 gene on chromosome 8q22.1.
Disease Node Iddisease_node_14969
Doid IdDOID_0111639
LabelAutosomal Recessive Nonsyndromic Deafness 109