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X-Linked Deafness 4

Disease ID: disease_node_14961

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DbxrefMIM:300066
SubclassofDOID_0050566
Data SourceDOID
SynonymsDFN6, DFNX4, X-linked progressive deafness 6, nonsyndromic sensorineural progressive deafness 6
Doid LabelX-linked deafness 4
Doid DescriptionAn X-linked nonsyndromic deafness characterized by progressive hearing loss with postlingual onset and earlier onset in males compared to females that has_material_basis_in mutation in the SMPX gene on chromosome Xp22.12.
Disease Node Iddisease_node_14961
Doid IdDOID_0111735
LabelX-Linked Deafness 4