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X-Linked Deafness 3

Disease ID: disease_node_14960

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DbxrefMIM:300030
SubclassofDOID_0050566
Data SourceDOID
SynonymsDFN4, DFNX3, congenital sensorineural X-linked deafness 4
Doid LabelX-linked deafness 3
Doid DescriptionAn X-linked nonsyndromic deafness characterized by congenital, bilateral, profound and sensorineural hearing loss in males and bilateral, mild to moderate high frequency sensorineural hearing impairment with later onset in heterozygous females that has_material_basis_in mutation in a region on chromosome Xp21.2.
Disease Node Iddisease_node_14960
Doid IdDOID_0111736
LabelX-Linked Deafness 3