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Primary Ciliary Dyskinesia 38

Disease ID: disease_node_14679

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DbxrefMIM:618063
SubclassofDOID_0050737, DOID_9562
Data SourceDOID
SynonymsCILD38, primary ciliary dyskinesia 38 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 38
Doid DescriptionA primary ciliary dyskinesia characterized by significant loss of both the inner and outer dynein arms, chronic airway disease, recurrent sinopulmonary infections, and laterality defects in about half of patients that has_material_basis_in homozygous or compound heterozygous mutation in the CFAP300 gene on chromosome 11q22.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_14679
Doid IdDOID_0111852
LabelPrimary Ciliary Dyskinesia 38