This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Primary Ciliary Dyskinesia 40

Disease ID: disease_node_14678

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:618300
SubclassofDOID_0050737, DOID_9562
Data SourceDOID
SynonymsCILD40, primary ciliary dyskinesia 40 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 40
Doid DescriptionA primary ciliary dyskinesia characterized by a subtle defect in the bend of the distal portion of the cilia, reduced ciliary clearance in-vitro, relatively mild respiratory phenotype and laterality defects in all reported patients that has_material_basis_in homozygous or compound heterozygous mutation in the DNAH9 gene on chromosome 17p12.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_14678
Doid IdDOID_0111853
LabelPrimary Ciliary Dyskinesia 40