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Primary Ciliary Dyskinesia 39

Disease ID: disease_node_14677

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DbxrefMIM:618254
SubclassofDOID_0050737, DOID_9562
Data SourceDOID
SynonymsCILD39, primary ciliary dyskinesia 39 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 39
Doid DescriptionA primary ciliary dyskinesia characterized by ciliary kinetic defects in some patients, chronic sinopulmonary infections beginning soon after birth and laterality defects in about half of patients that has_material_basis_in homozygous or compound heterozygous mutation in the LRRC56 gene on chromosome 11p15.5.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_14677
Doid IdDOID_0111854
LabelPrimary Ciliary Dyskinesia 39