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Primary Ciliary Dyskinesia 42

Disease ID: disease_node_14676

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DbxrefMIM:618695
SubclassofDOID_0050737, DOID_9562
Data SourceDOID
SynonymsCILD42, primary ciliary dyskinesia 42 without situs inversus
Doid Labelprimary ciliary dyskinesia 42
Doid DescriptionA primary ciliary dyskinesia characterized by severe reduction or absence of multiple motile cilia in respiratory epithelia, onset of respiratory insufficiency soon after birth, recurrent upper and lower respiratory infections, and absence of laterality defects that has_material_basis_in homozygous or compound heterozygous mutation in the MCIDAS gene on chromosome 5q11.2.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_14676
Doid IdDOID_0111855
LabelPrimary Ciliary Dyskinesia 42