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Primary Ciliary Dyskinesia 45

Disease ID: disease_node_14674

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DbxrefMIM:618801
SubclassofDOID_0050737, DOID_9562
Data SourceDOID
SynonymsCILD45, primary ciliary dyskinesia 45 without situs inversus
Doid Labelprimary ciliary dyskinesia 45
Doid DescriptionA primary ciliary dyskinesia characterized by absence of inner dynein arms with some axonemal disorganization in airway epithelial cells, absence of both inner and outer dynein arms in sperm from infertile male patients, recurrent sinopulmonary infections, defective mucociliary clearance, and absence of laterality defects that has_material_basis_in homozygous or compound heterozygous mutation in the TTC12 gene on chromosome 11q23.2.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_14674
Doid IdDOID_0111857
LabelPrimary Ciliary Dyskinesia 45