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Primary Ciliary Dyskinesia 41

Disease ID: disease_node_14673

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DbxrefMIM:618449
SubclassofDOID_0050737, DOID_9562
Data SourceDOID
SynonymsCILD41
Doid Labelprimary ciliary dyskinesia 41
Doid DescriptionA primary ciliary dyskinesia characterized by hyperkinetic ciliary beat patterns, defects in ciliary orientation, chronic sinusitis, otitis media, and bronchiectasis that has_material_basis_in homozygous or compound heterozygous mutation in the GAS2L2 gene on chromosome 17q12.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_14673
Doid IdDOID_0111858
LabelPrimary Ciliary Dyskinesia 41