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Primary Ciliary Dyskinesia 1

Disease ID: disease_node_14671

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DbxrefICD10CM:Q34.8, MIM:244400
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD1, primary ciliary dyskinesia 1 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 1
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer dynein arm defect and in about half of patients situs inversus and has_material_basis_in compound heterozygous mutation in the DNAI1 gene on chromosome 9p13.
Disease Node Iddisease_node_14671
Doid IdDOID_0110594
LabelPrimary Ciliary Dyskinesia 1