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Stromme Syndrome

Disease ID: disease_node_14670

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DbxrefICD10CM:Q87.8, MIM:243605
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD31, apple peel syndrome with microcephaly and ocular anomalies, jejunal atresia with microcephaly and ocular anomalies, lethal fetal brain malformation-duodenal atresia-bilateral renal hypoplasia syndrome, primary ciliary dyskinesia 31
Doid LabelStromme syndrome
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance and ciliopathy with some type of intestinal atresia, variable ocular abnormalities, microcephaly, and has_material_basis_in compound heterozygous mutation in the CENPF gene on chromosome 1q41.
Disease Node Iddisease_node_14670
Doid IdDOID_0110595
LabelStromme Syndrome