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Primary Ciliary Dyskinesia 14

Disease ID: disease_node_14667

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DbxrefICD10CM:Q34.8, MIM:613807
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD14, primary ciliary dyskinesia 14 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 14
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with inner dynein arm defect and axonemal disorganization, chronic upper and lower airway infections, and has_material_basis_in homozygous or compound heterozygous mutation in the CCDC39 gene on chromosome 3q26.
Disease Node Iddisease_node_14667
Doid IdDOID_0110598
LabelPrimary Ciliary Dyskinesia 14