This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Primary Ciliary Dyskinesia 3

Disease ID: disease_node_14666

Connections displayed (default: 10).
Loading graph...

DbxrefICD10CM:Q34.8, MIM:608644
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD3, primary ciliary dyskinesia 3 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 3
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer dynein arm defect, ciliary akinesia and variable occurence of situs inversus and has_material_basis_in homozygous or compound heterozygous mutation in the DNAH5 gene on chromosome 5p15.
Disease Node Iddisease_node_14666
Doid IdDOID_0110599
LabelPrimary Ciliary Dyskinesia 3