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Primary Ciliary Dyskinesia 12

Disease ID: disease_node_14664

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DbxrefICD10CM:Q34.8, MIM:612650
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD12, primary ciliary dyskinesia 12 without situs inversus
Disease Has FeatureDOID_9563
Doid Labelprimary ciliary dyskinesia 12
Doid DescriptionA primary ciliary dyskinesia that is characterized by reduced exercise tolerance, chronic wet cough, recurrent respiratory infections, bronchiectasis, and nasal symptoms, and has_material_basis_in homozygous mutation in the RSPH9 gene on chromosome 6p21.
Has SymptomSYMP_0000686, SYMP_0020027
Disease Node Iddisease_node_14664
Doid IdDOID_0110601
LabelPrimary Ciliary Dyskinesia 12