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Primary Ciliary Dyskinesia 32

Disease ID: disease_node_14663

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DbxrefICD10CM:Q34.8, MIM:616481
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD32, primary ciliary dyskinesia 32 without situs inversus
Doid Labelprimary ciliary dyskinesia 32
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with near absence of radial spokes, respiratory distress in term neonates, impaired mucociliary clearance, chronic respiratory infections, bronchiectasis, and infertility and has_material_basis_in homozygous or compound heterozygous mutation in the RSPH3 gene on chromosome 6q25.
Disease Node Iddisease_node_14663
Doid IdDOID_0110603
LabelPrimary Ciliary Dyskinesia 32