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Primary Ciliary Dyskinesia 7

Disease ID: disease_node_14661

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DbxrefICD10CM:Q34.8, MIM:611884
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD7, primary ciliary dyskinesia 7 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 7
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with chronic respiratory infections, chronic sinusitis, recurrent bronchitis, and pneumonia beginning in infancy or early childhood and has_material_basis_in mutation in the DNAH11 gene on chromosome 7p21.
Disease Node Iddisease_node_14661
Doid IdDOID_0110605
LabelPrimary Ciliary Dyskinesia 7