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Primary Ciliary Dyskinesia 28

Disease ID: disease_node_14659

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DbxrefICD10CM:Q34.8, MIM:615505
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD28, primary ciliary dyskinesia 28 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 28
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer and inner dynein arm defect, recurrent upper and lower airway disease, bronchiectasis, and decreased fertility and has_material_basis_in homozygous or compound heterozygous mutation in the SPAG1 gene on chromosome 8q22.
Disease Node Iddisease_node_14659
Doid IdDOID_0110607
LabelPrimary Ciliary Dyskinesia 28