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Primary Ciliary Dyskinesia 34

Disease ID: disease_node_14656

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DbxrefMIM:617091
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD34, primary ciliary dyskinesia 34 without situs inversus
Doid Labelprimary ciliary dyskinesia 34
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with childhood onset of recurrent sinopulmonary infections and male infertility and has_material_basis_in homozygous mutation in the DNAJB13 gene on chromosome 11q13.
Disease Node Iddisease_node_14656
Doid IdDOID_0110610
LabelPrimary Ciliary Dyskinesia 34