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Primary Ciliary Dyskinesia 27

Disease ID: disease_node_14655

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DbxrefICD10CM:Q34.8, MIM:615504
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD27, primary ciliary dyskinesia 27 without situs inversus
Doid Labelprimary ciliary dyskinesia 27
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with neonatal respiratory distress, recurrent upper and lower airway disease, and bronchiectasis and has_material_basis_in homozygous mutation in the CCDC65 gene on chromosome 12q13.
Disease Node Iddisease_node_14655
Doid IdDOID_0110611
LabelPrimary Ciliary Dyskinesia 27