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Primary Ciliary Dyskinesia 16

Disease ID: disease_node_14653

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DbxrefICD10CM:Q34.8, MIM:614017
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD16, primary ciliary dyskinesia 16 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 16
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with absence of ciliary outer dynein arms, early infantile onset of respiratory distress, and variable occurrence of situs inversus and has_material_basis_in homozygous mutation in the DNAL1 gene on chromosome 14q24.3.
Disease Node Iddisease_node_14653
Doid IdDOID_0110613
LabelPrimary Ciliary Dyskinesia 16