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Primary Ciliary Dyskinesia 4

Disease ID: disease_node_14652

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DbxrefICD10CM:Q34.8, MIM:608646
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD4, primary ciliary dyskinesia 4 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 4
Doid DescriptionA primary ciliary dyskinesia that is characterized by partial absence of the inner dynein arms with variable occurrence of situs inversus and has_material_basis_in variation in the chromosome region 15q13.1-q15.1.
Disease Node Iddisease_node_14652
Doid IdDOID_0110614
LabelPrimary Ciliary Dyskinesia 4