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Primary Ciliary Dyskinesia 25

Disease ID: disease_node_14651

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DbxrefICD10CM:Q34.8, MIM:615482
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD25, primary ciliary dyskinesia 25 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 25
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with inner and outer dynein arm defect, recurrent upper and lower airway disease, bronchiectasis, decreased fertility and variable occurence of laterality defects and has_material_basis_in homozygous or compound heterozygous mutation in the DYX1C1 gene on chromosome 15q21.
Disease Node Iddisease_node_14651
Doid IdDOID_0110615
LabelPrimary Ciliary Dyskinesia 25