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Primary Ciliary Dyskinesia 35

Disease ID: disease_node_14646

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DbxrefMIM:617092
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD35, primary ciliary dyskinesia 35 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 35
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with absent outer dynein arms, immotile cilia, variable occurence of laterality defects and recurrent upper and lower respiratory infections and has_material_basis_in homozygous mutation in the TTC25 gene on chromosome 17q21.
Disease Node Iddisease_node_14646
Doid IdDOID_0110620
LabelPrimary Ciliary Dyskinesia 35