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Primary Ciliary Dyskinesia 20

Disease ID: disease_node_14641

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DbxrefICD10CM:Q34.8, MIM:615067
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD20, primary ciliary dyskinesia 20 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 20
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with outer dynein arm defect, infantile onset of chronic sinopulmonary infections, and variable occurence of laterality defects and has_material_basis_in homozygous or compound heterozygous mutation in the CCDC114 gene on chromosome 19q13.
Disease Node Iddisease_node_14641
Doid IdDOID_0110625
LabelPrimary Ciliary Dyskinesia 20