This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Primary Ciliary Dyskinesia 2

Disease ID: disease_node_14640

Connections displayed (default: 10).
Loading graph...

DbxrefICD10CM:Q34.8, MIM:606763
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD2, primary ciliary dyskinesia 2 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 2
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with inner and outer dynein arm defect, otitis media, sinusitis, chronic cough, recurrent respiratory infections, and variable occurence of laterality defects and has_material_basis_in homozygous mutation in the DNAAF3 gene on chromosome 19q13.
Has SymptomSYMP_0000686
Disease Node Iddisease_node_14640
Doid IdDOID_0110626
LabelPrimary Ciliary Dyskinesia 2