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Primary Ciliary Dyskinesia 26

Disease ID: disease_node_14639

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DbxrefICD10CM:Q34.8, MIM:615500
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD26, primary ciliary dyskinesia 26 with or without situs inversus
Doid Labelprimary ciliary dyskinesia 26
Doid DescriptionA primary ciliary dyskinesia that is characterized by autosomal recessive inheritance with inner and outer dynein arm defect, neonatal respiratory distress, recurrent upper and lower airway disease, bronchiectasis, and variable occurence of laterality defects and has_material_basis_in homozygous or compound heterozygous mutation in the C21ORF59 gene on chromosome 21q22.
Disease Node Iddisease_node_14639
Doid IdDOID_0110627
LabelPrimary Ciliary Dyskinesia 26