This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Primary Ciliary Dyskinesia 11

Disease ID: disease_node_14637

Connections displayed (default: 10).
Loading graph...

DbxrefICD10CM:Q34.8, MIM:612649
SubclassofDOID_9562
Data SourceDOID
SynonymsCILD11, primary ciliary dyskinesia 11 without situs inversus
Disease Has FeatureDOID_9563
Doid Labelprimary ciliary dyskinesia 11
Doid DescriptionA primary ciliary dyskinesia that is characterized by reduced exercise tolerance, chronic wet cough, recurrent respiratory infections, bronchiectasis, nasal symptoms, ear obstruction with consequent hearing problems, low weight, and short stature, and has_material_basis_in homozygous or compound heterozygous mutation in the RSPH4A gene on chromosome 6q22.
Has SymptomSYMP_0000686, SYMP_0000475, SYMP_0020027
Disease Node Iddisease_node_14637
Doid IdDOID_0110602
LabelPrimary Ciliary Dyskinesia 11