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Acute Interstitial Pneumonia

Disease ID: disease_node_14548

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DbxrefGARD:12835, ICD10CM:J84.114, ICD9CM:516.33, NCI:C35806, ORDO:79126, SNOMEDCT_US_2023_03_01:129459004, UMLS_CUI:C1279945
SubclassofDOID_2797
Data SourceDOID
SynonymsAIP, Hamman-Rich disease, Hamman-Rich syndrome, Idiopathic pulmonary fibrosis, acute fatal form, accelerated interstitial pneumonia, acute interstitial pneumonitis
Doid Labelacute interstitial pneumonia
Doid DescriptionA idiopathic interstitial pneumonia which develops suddenly and is severe. Initially, the lung shows edema, hyaline membranes, and interstitial acute inflammation. Later, it develops loose organizing fibrosis, mostly within alveolar septa and type II pneumocyte hyperplasia. Fever, cough, and difficulty breathing develop over 1 to 2 weeks, typically progressing to acute respiratory failure.
Has SymptomSYMP_0000614
Disease Node Iddisease_node_14548
Doid IdDOID_2800
LabelAcute Interstitial Pneumonia