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Episodic Kinesigenic Dyskinesia 1

Disease ID: disease_node_14356

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DbxrefGARD:8721, ICD10CM:G24.8, MIM:128200, ORDO:98809
SubclassofDOID_0050736, DOID_543
Data SourceDOID
SynonymsParoxysmal kinesigenic choreoathetosis
Doid Labelepisodic kinesigenic dyskinesia 1
Doid DescriptionA dystonia characterized by recurrent brief involuntary hyperkinesias triggered by sudden movements that has_material_basis_in autosomal domit inheritance of heterozygous mutation in the proline-rich transmembrane protein 2 gene (PRRT2) on chromosome 16p11.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_14356
Doid IdDOID_0090053
LabelEpisodic Kinesigenic Dyskinesia 1