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Ataxia Telangiectasia

Disease ID: disease_node_1426

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DbxrefGARD:5862, MESH:D001260, MIM:208900, NCI:C2887, SNOMEDCT_US_2023_03_01:68504005, UMLS_CUI:C0004135
SubclassofDOID_0050950
Data SourceDOID, MESH
SynonymsBoder-Sedgwick syndrome, Louis Bar syndrome
Mesh IdD001260
Mesh LabelAtaxia Telangiectasia
Mesh SubclassofD020752, D013684, D020754, D030342, D049914, D000081207
Doid Labelataxia telangiectasia
Doid DescriptionAn autosomal recessive cerebellar ataxia that is characterized by cerebellar ataxia, telangiectases, immune defects, and a predisposition to maligcy and that has_material_basis_in homozygous or compound heterozygous mutation in the ATM gene on chromosome 11q22. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_1426
Doid IdDOID_12704
LabelAtaxia Telangiectasia